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Dysferlin蛋白抗體,Anti-Dysferlin抗體

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“Dysferlin蛋白抗體,Anti-Dysferlin抗體"應用于IHC、WB、 IF、IP、ELISA,質(zhì)量保證,無效免費退換,另外本公司生產(chǎn)經(jīng)營各種標記二抗、免疫印跡常用試劑、免疫組化常用試劑,咨詢!

Dysferlin蛋白抗體,Anti-Dysferlin抗體”應用于IHC、WB、 IF、IP、ELISA,質(zhì)量保證,無效免費退換,另外本公司生產(chǎn)經(jīng)營各種標記二抗、免疫印跡常用試劑、免疫組化常用試劑,咨詢!

產(chǎn)品介紹:

【產(chǎn)品名稱】:Dysferlin蛋白抗體,Anti-Dysferlin抗體

【產(chǎn)品類型】:一抗


【產(chǎn)品編號】:BYk-2429R                    

【相關(guān)標記】: HRP Biotin Gold RBITC AP FITC Cy3 Cy5 Cy5.5 Cy7 PE PE-Cy3 PE-CY5 PE-CY5.5 PE-CY7 APC Alexa Fluor 350 Alexa Fluor 488 Alexa Fluor 555 Alexa Fluor 647


【性 狀】: Lyophilized or Liquid


【濃 度】: 1mg/1ml


【亞 型】: IgG


【規(guī) 格】:0.1ml/100ug,0.2ml/200ug


【抗體來源】: Rabbit OR MOUSE


【克隆類型】: polyclonal or monoclonal

【產(chǎn)品用途】:科研實驗,用于免疫組化實驗,WB實驗、IF、IP、ELISA實驗,相應的標記抗體有HRP標記抗體,F(xiàn)ITC標記,BIO等。


【貯 存】: Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
Important Note This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.


【信息詳情】: The protein encoded by this gene belongs to the ferlin family and is a skeletal muscle protein found associated with the sarcolemma. It is involved in muscle contraction and contains C2 domains that play a role in calcium-mediated membrane fusion events, suggesting that it may be involved in membrane regeneration and repair. In addition, the protein encoded by this gene binds caveolin-3, a skeletal muscle membrane protein which is important in the formation of caveolae. Specific mutations in this gene have been shown to cause autosomal recessive limb girdle muscular dystrophy type 2B (LGMD2B) as well as Miyoshi myopathy. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Aug 2008].

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